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- PicoProbe™ D-2-Hydroxyglutarate Dehydrogenase Assay Kit (Fluorometric)
Biovision
PicoProbe™ D-2-Hydroxyglutarate Dehydrogenase Assay Kit (Fluorometric)
- SKU:
- 26-K248
- UPC:
- MPN:
- Availability:
- Usually Shipped in 5 Working Days
- Size:
- 100 Assays
- Storage Conditions:
- -20°C
- Shipping Conditions:
- Gel Pack
- Shelf life:
- 12 months
Description
D-2-Hydroxyglutarate Dehydrogenase (D2HGDH: EC 1.1.99.2) is a mitochondrial enzyme which catalyzes the conversion of D-2-Hydroxyglutarate into 2-Oxoglutarate. In humans, mutation of D2HGDH gene could reduce D2HGDH activity which will cause the D-2-Hydroxyglutarate accumulation in body fluids. Increased D-2-Hydroxyglutarate level in body fluids leads to D-2-Hydroxyglutaric Aciduria, a neurometabolic disorder characterized as developmental delay, epilepsy, hypotonia, and dysmorphic features. BioVision’s PicoProbe™ D-2-Hydroxyglutarate Dehydrogenase Assay kit provides a quick and easy method for monitoring D2HGDH activity in a wide variety of samples. In this assay, D2HGDH converts D-2-Hydroxyglutarate into 2-Oxoglutarate and NADH, which further reduces PicoProbe™ to generate an intense fluorescent product (Ex/Em = 535/587 nm). This kit is simple, sensitive and high-throughput adaptable and can detect as low as 4 µU/µl of D2HGDH activity.
Alternate Name: N/A
Tag Line: Rapid, sensitive & simple assay to measures D-2Hydroxyglutarate Dehydrogenase activity
Summary: • Detection method- Fluorescence (Ex/Em=535/587 nm) • Application- Detection of D-2-Hydroxyglutarate Dehydrogenase activity
Detection Method: Fluorescence (Ex/Em=535/587 nm)
Sample Type: • Purified recombinant protein • Cell and tissue lysate
Species Reactivity: Mammalian
Applications: Detection of D-2-Hydroxyglutarate Dehydrogenase activity
Features & Benefits: • Rapid, sensitive and convenient • The kit measures total Activity of D-2-Hydroxyglutatare Dehydrogenase Activity with limit of quantification 4 µU/µl using recombinant D2HGDH
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